Insulinoma and Isolated Polycystic Liver Disease: Case Report

Gastroenteropancreatic neuroendocrine tumors are fairly rare neoplasms and their diagnosis can result defying. Polycystic liver disease is also a rare condition characterized by the formation of liver cysts. We report a case of a 59-year-old female with isolated polycystic liver disease and hypoglycemia. The prolonged diagnostic fast indicated the presence of endogenous hyperinsulinism and after distal pancreatectomy the final histological result confirmed the presence of an insulinoma. The coexistence of these two unusual clinical conditions was unexpected and there are few reported cases associating both conditions.